A CASE OF LOCALIZED IGG4-RELATED PERIAORTITIS AND VOCAL CORD PALSY

Dr.Sivaraman A; Dr.Ajay Narasimhan; Dr.Aravind Moorthy

Volume : VII, Issue : X, October - 2018

A CASE OF LOCALIZED IGG4-RELATED PERIAORTITIS AND VOCAL CORD PALSY

Dr. Sivaraman A, Dr. Ajay Narasimhan, Dr. Aravind Moorthy

Abstract :

IGG4-related disease is a newly recognized idiopathic sclerosing lesions with wide spectrum of manifestations starting with autoimmune pancreatitis (AIP) ,a specific type of chronic pancreatitis and an original member of the IgG4-RD family ,sclerosing cholangitis,sialoadenitis,retroperitoneal fiosis,tubulointerstitial nephritis etc. In this report, we describe a case of a 31-yearold man with marked periaortic fious thickening localized to the aortic arch initially presented only as vocal cord palsy. Histologic examination revealed infiltration of lymphoplasmacytes and marked fiosis with numerous IgG4-positive plasma cells which are hallmark of this disease. The serum concentration of IgG4 was 263 mg/dL,Twice the normal value.Treatment with steroid is well proven for this spectrm of disorder.