Low-Grade Fibromyxoid  Sarcoma�A Case Report and Review of Literature

Volume : VI, Issue : III, March - 2017

M . K. Paswan, M . A. Ansari, A. K. Shrivastav

Low-grade fiomyxoid sarcoma (LGFMS) is a rare neoplasm with a tendency

to develop in deep soft tissue of young adults.⁽¹⁾ It is also referred to as �Evans

tumor�, �Hyalinizing spindle cell tumor with giant rosettes� and �Low-grade

fiosarcoma with palisaded granuloma like bodies�.^(2,3) LGFMS is considered a

diagnostic dilemma because of its innocuous and varied histological features that

can be potentially confused with other benign or low-grade fiomyxoid lesions.

This report is aimed at reinforcing the need to recognize LGFMS as a sarcoma

despite its deceptively benign histological appearance.

Case Report:

A 20-year-old female patient presented to the surgery Out Patient Department

with a painless, deeply situated mass in the proximal extremity (right forearm),

present for 5 years. Patient was referred to the pathology department for

Fine Needle Aspiration Cytology (FNAC). FNAC was suggestive of a benign

mesenchymal lesion of neural or fioblastic origin. This was followed by excision.

Pathological examination of the excised swelling revealed a grossly circumscribed,

Unencapsulated tumor measuring 8 x5 x3 cms in size. The cut surface varied from

being gray white, firm and fious to gelatinous or myxoid. Microscopy revealed

cellular areas constituted by bland spindle shaped fioblasts, alternating with less

cellular myxoid areas. A typical pattern of intermixed, sweeping bands of fious and

myxoid tissue, focal areas of storiform architecture and concentric perivascular

cuffs of slender spindle cells was seen ( Figure 1 ).