Dandy Walker Malformation with Parietal Encephalocele– Case Report.

Dr Vikram Shende; Dr Punit Agrawal; Dr Santosh Konde; Dr Hariqbal Singh

Volume : VI, Issue : III, March - 2016

Dandy Walker Malformation with Parietal Encephalocele– Case Report.

Dr Vikram Shende, Dr Punit Agrawal, Dr Santosh Konde, Dr Hariqbal Singh

Abstract :

 Dandy–Walker malformation is congenital malformation characterized by dysgenesis of the foramina of Magendie & Lushka in the upper 4th ventricle, hypoplasia of the cerebellar vermis and agenesis of the corpus callosum. Cephaloceles are congenital malformations with herniation of intracranial structures through a defect in the cranium. It is one of the rarest neural tube defect. A 3 year old male child came with 2x2 cm encephalocele on physical examination. On magnetic resonance imaging, the posterior fossa was enlarged with cysts and vermian hypoplasia. A connection was seen between the ventricle and the cysts in the posterior fossa. These findings were significant from the aspect of Dandy–Walker malformation. Bony defect in the right parietal region with extension reaching 7 mm was seen in accordance with encephalocele. It is rare for Dandy–Walker syndrome to occur together with parietal encephalocele.