CASE OF HEMICONVULSION HEMIPLEGIA EPILEPSY SYNDROME ASSOCIATED WITH INFLAMMATORY- DEGENERATIVE IMAGING FINDINGS IN A TODDLER WITH ADRENAL INSUFFIENCY.

CH.MITHUN REDDY; ARMEL ARPUTHA SIVARAJAN

Volume : IX, Issue : IV, April - 2020

CASE OF HEMICONVULSION HEMIPLEGIA EPILEPSY SYNDROME ASSOCIATED WITH INFLAMMATORY- DEGENERATIVE IMAGING FINDINGS IN A TODDLER WITH ADRENAL INSUFFIENCY.

Ch. Mithun Reddy, Armel Arputha Sivarajan

Abstract :

Hemiconvulsion–Hemiplegia–Epilepsy (HHE) syndrome is an uncommon outcome of prolonged focal status epilepticus in childhood usually occurring during feile illness followed by hemiplegia ipsilateral to the side of convulsions which is associated with seizures, cereal holo–hemispheric global atrophy of one hemisphere and transient or permanent epilepsy. This is a report of 4 year male child with right sided hemiparesis, vacant stare and adrenal insufficiency with past history of altered sensorium and focal dyscognitive seizures. This is accompanied by radiologic evidence of acute cytotoxic edema in the affected hemisphere followed by chronic atrophy. MRI ain shows gliosis, restricted diffusion in the left cereal hemisphere and with reduced caliber of he left ICA, anterior, middle and posterior cereal arteries.