BACKGROUND: Dieulafoy‘s lesion is an uncommon but important cause of recurrent upper gastrointestinal bleeding. Extragastric location of Dieulafoy‘s lesion is very rare. We report a case of Dieulafoy‘s lesion of the Terminal ileum Discussion and Result : The appropriate evaluation of small bowel bleeding, an aggressive multidisciplinary approach, such as radiologic intervention, enteroscopy, clips application and surgery, should be performed. Our case  was successfully controlled with endoscopic treatment by clips application CONCLUSIONS  : The Dieulafoy‘s lesion of the terminal ileum is extremely  rare and can be associated with massive, life–threatening hemorrhage . With advances in endoscopic techniques, enteroscopy could play a major role in the diagnosis and treatment of ileal Dieulafoy lesion bleeding.