Head and neck paragangliomas (HNPs) are tumors of the autonomic system. They arise from chromaffin cells of the parasympathetic paraganglia of the skull base and neck, and are also called glomus tumors [1–5]. Paraganglia are chemoreceptor organs that are distributed throughout the body. They include glomus jugulare and glomus tympanicum within the temporal bone, carotid body tumors arising from the carotid body and also along nerves in the head and neck like the vagus and laryngeal nerves.