Much confusion exists in literature regarding the relationship between Kimura’s disease and angiolymphoid hyperplasia with eosinophilia (ALHE). They were initially thought to represent the same disease spectrum, but it has now been widely accepted that they are unrelated and represent different entities.The former represents a benign vascular tumor and the latter represents a lymphoid hyperplasia. Recognition of the clinical characteristics and histological features of Kimura’s disease and ALHE is very important in making this distinction. We evaluated the clinical and histopathologic features of ALHE and Kimura’s disease in our patients and also reviewed the differences between ALHE and Kimura’s disease to emphasize that they are two distinctive entities.