Parry Romberg Syndrome is a rare disorder of suspected Autoimmune Etiology. First Described by Parry in 1825 and Romberg in 1846. Eulenberg in 1871 termed it  as Progressive facial hemi atrophy. The syndrome is characterised by slow atrophy involving one side of face. The affected individuals are normal at birth, with insidious atrophy progression   in first two Decades of life.. We Report  a unique case of   9 years  girl with parry Romberg syndrome with no neurological sequalae  but with  hypo plastic maxillary bones, malocclusion of teeth, atrophy of tongue hepatosplenomegaly  and failure  to thrive.