Congenital cystic adenomatoid malformation (CCAM) is a rare congenital hamartomatous malformation of lung with incidence 1 in 2500 to 1 in 3500 live births. In this case report, we discuss type 1 Congenital Cystic Adenomatoid Malformation in 5 year old male child who presented with complains of recurrent attack of cough and respiratory distress since 2 months after birth. Radiological examination confirmed the diagnosis. Patient was treated with lobectomy.Histopathological examination reported the diagnosis of type1 Congenital Cystic Adenomatoid Malformation. Background: