Primitive neuroectodermal tumors (PNETs) are malignant, poorly differentiated neoplasms derived from the neural crest. Only a few cases of primary intraspinal PNETs have been reported in children and in adults. Here, we present a case study of a 44–year–old female with L3 intradural PNET grade IV, including details of her examination, surgical procedures applied, histological findings and her subsequent treatment.Post operative neurological improvement was minimal. Primary intraspinal PNETs are rare tumors and carry a poor prognosis.