The term ‘Malignant Extrarenal Rhabdoid Tumor (MERT)’ is used for those tumors occurring in extrarenal locations. Since the initial description, only a few cases of MERT involving the anorectum have been reported in the literature and none has been reported in the radiology literature to our knowledge. Here, we report on the computed tomography, magnetic resonance imaging and ultrasonographic features of a rare case of malignant rhabdoid tumor of the anorectum in a 53 year old female patient. To our understanding, this is the first case report of MERT involving the anorectum that includes imaging features. MERTs present as very aggressive neoplasms at the time of diagnosis thus have poor prognosis. Radiologists should be aware of the imaging findings of the MERT of the anorectum and include it as a differential diagnosis when there is as a large, heterogeneous tumor involving the anorectum.