Objective: To study the clinical presentations of nasal dermoids in children and adults and discuss its management.

Design: Retrospective study

Setting: Tertiary care hospital

Patients and methods: A total of 5 cases of nasal dermoids were studied and successfully treated.

Results: The average age of presentation was 6.2 years. The most common clinical presentation was a sinus pit with tuft of hair (n=3). Others included ill defined midline swelling of the nose, swelling at the fronto–nasal angle, and a medial canthal sinus. All patients underwent imaging work up. None of the patients showed radiological evidence of intracranial extension. No patient presented with recurrence. Final aesthetic outcome was satisfactory.

Conclusion: Nasal dermoid is a rare and cosmetically concerning congenital anamoly. Radiology helps to exclude multiple tracts and evidence of intracranial extension. Surgery and incision depends upon extent and position of lesion. Combined intracranial extracranial approach may be needed for extensive lesions. Recurrence is uncommon.