Xeroderma pigmentosum (XP), meaning parchment skin and pigmentary disturbance, is a rare and mostly autosomal recessive genetic disorder. The frequency of this disease in the general population of the U.S.A. is 1:250,000. It is characterized by a genetic defect in DNA repair. The consequence is a high incidence of skin cancers on sun–exposed cutaneous surfaces of affected children. First lesions appear in the first years of life: telangiectasia, actinic keratosis and keratoacanthomas. Squamous cell carcinoma , basal cell carcinoma,  malignant melanoma are the most frequent neoplasms and rarely fibrosarcoma.We hereby report a rare case of 20 year old male affected by xeroderma pigmentosum, with manifesting as unusual skin malignancy– basosquamous carcinoma.