Introduction: The Herlyn–Werner–Wunderlich syndrome is a rare, congenital disorder characterised by uterus didelphys, unilateral obstructed hemivagina and ipsilateral renal agenesis, all being secondary to mesonephric duct–induced Mullerian anomalies. It is also known as obstructed hemivagina and ipsilateral renal anomaly (OHVIRA). It is generally observed in post–menarche adolescents and young women with dysmenorrhea, irregular menses, abdominal pain and pelvic mass.

Case report: A 14 years old Unmarried girl presented with complaints Pain in left illiafossa since 3 months white discharge Per vaginum since 3 days, pain during defecation since 3 months and bed weating (At night) since childhood.she had regular menstrual periods. She was admitted at Rajkot civil hospital from 30/1/2015 to 17/02/2015 for heamatocolpos and haematometra and hydrosalpinx and managed conservatively and was on oral antibiotics tablet doxycycline. Her MRI (6/10/2015) showed Bicornuatebicollis, Uterine didelphys cannot be ruled out. Large collection detected at vaginal cavity with gross dilatation of cavity and also extending to left side cervical and uterine cavity with its mild dilatation. Both ovaries appears normal. Mild ascitis. Left Kidney appears ectopic at left iliac fossa with altered axis with gross dilatation of PC system and visible ureter. Her vitals were normal and on abdominal examination soft swelling in left iliac fossa was felt. On per speculum, soft collection in vagina seen and on per rectum examination, soft bulking felt 10*8cm felt anteriorly. Incision and drainage done .under short general anaesthesia. A curvilinear incision kept over bulging area chochlate material drained and no active bleeding present. Diagnostic laproscopy was done and Dye test performed no spillage on left tube found. Few adhesions present between left ovary and left tube. Dissected with sharp scissor. Patient had given injectable antibiotics after procedure for 7 days and then patient discharged with no complaints.