Primary hydatid disease of the spleen is a very rare condition. Usually splenic hydatid cysts are secondary, resulting from either spontaneousspread of cysts or occurring after surgeries involving hydatid cysts in other regions.Even in the endemic region, thefrequency is reported to be 0.5–4% of abdominal hydatid diseases ^[8].The most common sites of hydatid disease are the liver (60–70%),acting as a first filter followed by the lungs (10–40%), which acts assecond filter. The other rare sites include spleen,kidney, thyroid, gall bladder,central nervous system and retroperitoneal region.

We report acase of a primary isolated hydatid cyst of spleen treated by a classical surgical approach. This case reportand literature review describes the management of splenic hydatidosis.