Breast sarcomas accounts only 1% of all malignant tumors of the breast, among which only 5% – 10% are leiomyosarcomas. LMS commonly noticed in 45–55 year age group people with almost similar presentation like other stromal tumors of breast.

It is difficult to diagnose leiomyosarcoma preoperatively as excision biopsy and immunohistochemistry are essential for the final diagnosis. Due to the rarity of the disease the treatment for LMS is not standardized. However excision of the tumor either by lumpectomy or simple mastectomy with wide clear margins and adjuvant radio therapy to the chest wall is considered as the optimal treatment.