she presented with marfanoid features.SP was managed with Intercostal chest tube drainage and Video assisted thoracic surgery. Marfan

Syndrome itself and its respiratory manifestastions are not common , hence patients who are clinico–etiologically suspicious of spontaneous

pneumothorax, marfan syndrome as a probable etiology should be kept in mind .

Background :–Spontaneous pneumothorax (SP) is a relatively rare condition in paediatric population with a bimodal peak age of occurance either

in neonatal period or in late adolescence. In children SP is often caused by a tear in visceral pleura due to rupture of a subpleural bulla & often affects

tall individuals with thin built1.

Marfan syndrome is a common inherited connective tissue disorder with typical skeletal, ocular and cardiovascular manifestations. Pulmonary

involvement occurs less frequently, with SP being the most frequently reported (4–11%)2–4.

Marfan syndrome should be suspected in patients with SP and marfanoid habitus.