Congenital atresia of coronary artery is a rare disease. We report a case of congenital coronary anomaly in a 3 year old male child. Patient was admitted with symptoms of heart failure. Echocardiography revealed a dilated heart. A diagnosis of Dilated cardiomyopathy was made (? Post myocarditis). Further coronary angiography showed atresia of left coronary artery as a cause of dilated cardiomyopathy.