Russell–Silver Syndrome (RSS) is a hetergenous syndrome which is characterized by severe intrauterine and postnatal growth retardation and typical dysmorphic features. The clinical picture is extremely diverse due to numerous diagnostic features reflecting a heterogeneous genetic disorder. It is a syndromic disorder present at birth that involves poor growth, low birth weight, short stature and differences in the size of the two sides of the body. This case report presents a dental management of an eleven year old female patient with Russell–Silver Syndrome