Allgrove syndrome is a Described by Allgrove et al in 1978, Allgrove syndrome consists of triad:ACHLASIA CARDIA,ADRENAL INSUFFICIENCY,ALACRIMIA. Allgrove syndrome is also known as Triple–A–Syndrome.Rareautosomal recessive disorder. Very few cases of this syndrome have been reported in literature.Usually cases present with symptoms in 1^st decade of life.Other features that have been reported in association with Allgrove syndrome include microcephaly, short stature, dysmorphicfeatures , palmar and plantar hyperkeratosis, osteoporosis, and long QT syndrome.