Bicuspid aortic valve (BAV) is an inherited form of heart disease in which two of the leaflets of the aortic valve fuse during development in the womb resulting in a six–leaflet valve (bicuspid valve) instead of the normal nine–leaflet valve (tricuspid). BAV is the most common cause of heart disease present at birth and affects approximately 1.3% of adults. Here I present a case of congenital bicuspid aortic valve who also had a ascending aortic aneurysm and needed surgery due to the large diameter of the aneurysm