Background:

Pseudomyxoma peritonei (PMP) is a very rare tumour characterized by deposition of gelatinous mucin in the abdominal cavity and peritoneal surface of the abdominal viscera. It usually arises from primary mucinous neoplasm of the appendix. The primary lesion can also be present in colorectum or rarely urachus. According to WHO 2010, PMP is classified into low grade and high grade. Most common primary tumour is low grade appendiceal mucinous neoplasm (LAMN). The histological appearance can range from paucicellular lesion with bland cellular features to those exhibiting frank adenocarcinoma. This case is presented due to its rarity.