Background: Congenital heart disease (CHD) is one of the major causes of mortality and morbidity in the pediatric population of both the developing and developed countries. Early detection of congenital heart disease is important to prevent mortality and morbidity among CHD patients. Aim was to study the prevalence, age and sex wise distribution, and clinical spectrum of congenital heart diseases (CHDs) at Department of pediatrics SGGIM&HS, Patel Nagar, Dehradun, India. Methods: Around 28620 children from birth (completed gestation age ≥37week) to 18 years were screened for congenital heart defects. Clinical examination and NADAS criteria were used for screening patients for CHDs, patients suggestive of CHD were evaluated using echocardiography and color Doppler as diagnostic tools. Results: A prevalence of 7.5 per 1000 population was observed. PDA (patent ductus arteriosus) in 36.7 % was the commonest lesion followed by VSD (ventricular septal defect) 28.9% and ASD (atrial septal defect) in 22.2%. Tetralogy of Fallot 69.4% was the commonest among cyanotic heart diseases. Maximum numbers of children with heart disease were diagnosed in the age group 0 to 6 weeks. Conclusions: For better estimation of prevalence of congenital heart diseases, more elaborate community and hospital based studies are needed. Community based studies can be done easily. Community screening programs helps in detecting silent cardiac ailments, their prevalence and pattern, and early therapeutic intervention. A few prevalence studies have been carried out in piecemeal manner in different locations of India; and more such studies are required to be conducted for estimation of the CHD load in community, required for policy formulation and implementation.