IJSR International Journal of Scientific Research 2277 - 8179 Indian Society for Health and Advanced Research ijsr-8-9-21875 Original Research Paper The study of HRCT and MRI Temporal bone findings in Pediatric patients with Congenital Sensorineural hearing loss Manish Bhagat Dr. Dr Garima Agrawal Varshney Dr. September 2019 8 9 01 02 ABSTRACT

Introduction –The incidence of Congenital Sensorineural hearing loss (SNHL) is approximately 1: 1000 live births. SNHL is either due to disorders of the inner ear or cochleovestibular cranial nerve. Radiological evaluation is necessary to detect or rule out causes of SNHL. Also, the treatment of SNHL is predominantly determined by the etiology of hearing loss. Aim & objective– Radiological assessment of various congenital inner ear malformations in pediatric age group patients with sensorineural hearing loss in a tertiary care centre. Material & Methods–This is a prospective study conducted between 1 February 2019 and 1 July 2019 in Department of Radiodiagnosis, SAIMS, Indore & included all paediatric patients (93 children), who came for HRCT and MRI temporal bone imaging with the clinical diagnosis of congenital sensorineural hearing loss (SNHL) / for evaluating congenital sensorineural hearing loss (SNHL). Results– In our study out of 93 paediatric patients , no significant radiological abnormality were detected in 68 patients (73.11%), however, 25 patients (26.88%) had various congenital anomalies of the inner ear and vestibulocochlear nerve. Most commonly affected organ was cochlea. Among these 25 patients only cochlea was involved in 7(28%), both Cochlea and semicircular canal in 4(16%), and Cochlea and vestibular aqueduct in 1 patient(4%). Isolated vestibular aqueduct dilatation was found in 8 (32%) patients. Isolated semicircular canal involvement and cochleovestibular nerve abnormality were seen in 3 (12%) and 2 (8%) patients respectively. Conclusion– In this study, imaging has helped us to detect various inner ear malformations in children with congenital sensorineural hearing loss. It is helpful for preoperative planning and preparation for cochlear implant in a tertiary care centre.