Congenital granular cell tumour (CGCT), an unusual benign mucosal lesion occurring in the oral cavity in infants, was first described in 1871. CGCT presents at birth as a mass over the gingival mucosa of the mandible or maxilla, with a marked female preponderance. Although benign, they usually interfere with respiration and feeding, necessitating early intervention. A two–day–old male child presented with a mass protruding from his mouth. It was surgically resected and diagnosed as CGCT on histopathology. Recommended management for CGCT is early surgical resection, which can be performed under local anaesthesia. Removal of the tumour facilitates complete mouth closure leading to proper feeding and respiration.