The Gorlin–Goltz syndrome (GGS) (the nevoid basal cell carcinoma syndrome—NBCCS) is a rare autosomal dominant syndrome caused due to mutations in the PTCH (patched) gene found on chromosome arm 9q. The syndrome, characterized by increased predisposition to develop basal cell carcinoma and associated multiorgan anomalies, has a high level of penetrance and variable expressiveness. This case report is of 29 years old male with complaint of pus discharge from upper and lower posterior teeth region since 5 months. On the basis of clinical and radiographic findings provisional diagnosis was made of gorlin –goltz syndrome and was planned for surgical intervention .But the patient deferred the treatment due to financial crisis .patient is recalled after 6 months for follow up.