Congenital Cystic Adenomatoid Malformation of the lung (CCAM) is a form of congenital cystic lung disease resulting from arrest in fetal lung development1. These were once considered the exclusive domain of the surgeon, who had the authority to operate on all congenital cystic lung abnormalities regardless of size or clinical signs in order to avoid the risk of cancer and improve lung growth in even asymptomatic infants2. Clinicians are reconsidering this approach in the light of the spontaneous improvement and possible resolution that occurs over months to years with many of these lesions, thinking about the opportunity to take a more conservative approach in many minimally symptomatic or asymptomatic infants in the early months of life2. The risks of subsequent cancer are poorly understood and probably overstated2. Many centers advocate surgery only in cases of symptomatic or significant lesions, although there is little consensus as to what constitutes a significant lesion2. This article aims to evaluate a neonate, born in our hospital and was antenatally diagnosed with CCAM. This study also focuses on follow–up of the infant during infancy, with an aim to assess the progression and intervene, if clinically needed.