Introduction: A congenital melanocytic nevus (CMN) is a lesion present at birth and containing nevus cells. Congenital nevi are rare and found in about 1% to 2% of newborn infants and are usually solitary. The appearance varies considerably on the basis of morphology, texture, location, and size. Clinically, congenital melanocytic nevi are classified on the basis of their size. Large or giant congenital melanocytic nevi are those which are 20 cm or more in greatest diameter. The term neurotization refers to the resemblance of some melanocytic cells to peripheral nerve sheath cells. In neurotization there is presence of elongated or slender melanocytes (exaggeration of the type C melanocytes) with fibrillary cytoplasm, often in the mid to deep portions of some nevi. Although neurotisation may be seen in giant congenital melanocytic nevi, it has not been reported in the Nongiant type