Nevus lipomatosus cutaneous superficialis (NLCS) is a rare benign hamartomatous skin tumor characterized by dermal deposition of mature adipose tissue. It was first described by Hoffmann and Zurhelle (1) in 1921. Clinically it is classified into two clinical subtypes: a multiple form and a solitary form. The lesions are usually found in the flank, buttocks, and upper part of the posterior aspect of the thigh, but they can occur on the abdomen, chest, and face.(2) We report a case of NLCS present in the left axillary region because of its rarity and its unusual site.