IJSR International Journal of Scientific Research 2277 - 8179 Indian Society for Health and Advanced Research ijsr-9-6-25568 Original Research Paper PRIMARY ORBITAL NEUROBLASTOMA- A RARE OCCURRENCE Pranab Mandal Dr. Chhanda Das Dr. June 2020 9 6 01 02 ABSTRACT

Neuroblastoma is derived from the sympathogonia of neural crest origin. It represents as the fourth most common tumor in the first decade of life as well as second most common orbital tumor in childhood. We report a rare case of primary orbital neuroblastoma in a 6–year–old girl. She presented with painless, rapid onset proptosis of the right eye for the past four months. Computed tomography and MRI study of orbit showed enhancing soft tissue lesion measuring 26x16x15 mm into middle cranial fossa and right orbit, compressing the temporal lobe, extraocular muscles, optic nerve, causing protrusion of right optic globe. A definite diagnosis of neuroblastoma was made. Additional medical assessment comprising of chest X–ray, CECT whole abdomen showed no systemic involvement. The diagnosis of primary orbital neuroblastoma was confirmed. Primary orbital neuroblastoma even though an unusual tumor in children should be taken into account as the differential diagnosis of orbital tumors in childhood