HENOCH SCHONLEIN PUPURA: A RARE CASE REPORT

B.Nadia Shulamite; Dr. G. Ramya Bala Prabha; Sharadha Srikanth; Konde Abbulu

Volume : VIII, Issue : IV, April - 2019

HENOCH SCHONLEIN PUPURA: A RARE CASE REPORT

B. Nadia Shulamite, Dr. G. Ramya Bala Prabha, Sharadha Srikanth, Konde Abbulu

Abstract :

Introduction: Henoch Schonlein purpura (HSP) is the most common vasculitis in children, in whom prognosis is mostly Dependent upon the severity of renal involvement.HSP mainly affects children between 4 to 15 years and has an incidence of 14 in 100,000 population with peak incidence at 5years. It usually involves skin, gut, joints, and kidneys. Nephritis is observed in about 30% of children with HSP. Renal damage eventually leads to chronic kidney disease in upto 20% of children.HSP nephritis and IgA nephropathy are related diseases resulting from glomerular deposition of aberrantly glycosylated IgA1. Discussion: A fourteen year old boy ,was diagnosed with Henoch Scholein purpura, IgA vasculitis with leucocytoclistic vasculitis. The patient complained about swelling of both legs since two days, and there was pain in joints , both the knees, ankles, wrist, metacarpal Since two days, rashes over both the legs , the rashes first started over feet ascending over legs and buttocks within a day , history of pain in abdomen, and burning type of pain in epigastrium region, increased frequency of urination. Patient experienced similar complaints four years back. A Clinical diagnosis of Henoch Scholein purpura, IgA vaculitis, leucocyttoclistic vasculitis was done. During the hospital administration, patient was managed symptomatically for pain control, skin rashesand electrolytes balance and corticosteroids were given to reduce the inflammation and thus treating rashes.. Conclusion: HSP is an autoimmune leucocytoclastic vasculitis of childhood which involves skin, gut, joints, and kidneys commonly.Most affected children have been between 2 and 11 years of age. Perioperative management of liver and kidney functions is important