LAPAROSCOPIC BARIATRIC SURGERY IN PRADER WILLI SYNDROME: ANAESTHESIA CONCERNS

JYOTI RAGHUWANSHI; ATUL DIXIT

Volume : VIII, Issue : X, October - 2019

LAPAROSCOPIC BARIATRIC SURGERY IN PRADER WILLI SYNDROME: ANAESTHESIA CONCERNS

Jyoti Raghuwanshi, Atul Dixit

Abstract :

Prader–Willi syndrome (PWS) is a rare complex multisystem genetic disorder of chromosome 15 resulting in physical, mental, and behavioural problem, especially unrelenting feeling of hunger causing morbid obesity. Anaesthesia concerns of PWS include morbid obesity, the potential for difficulties with airway management, risk for peri–operative respiratory failure, abnormalities in the central control of ventilation and temperature, rare reports of primary myocardial involvement, aggressive and at times violent behaviour and glucose intolerance. We present here the anaesthetic management of a 14–year–old female patient with Prader–Willi Syndrome, associated with morbid obesity (BMI 47.39), mild mental retardation, hypothyroidism and obstructive sleep apnoea syndrome, who was scheduled to undergo laparoscopic bariatric surgery. Anaesthetic considerations are reviewed highlighting perioperative complications associated with this syndrome.