VARIANT OF HERLYN WERNER WUNDERLICH SYNDROME - A RARE MULLERIAN DUCT ANAMOLY

Dr.K.RAMALINGAM; DR.K.SRI SOWMYA

Volume : VIII, Issue : VIII, August - 2019

VARIANT OF HERLYN WERNER WUNDERLICH SYNDROME - A RARE MULLERIAN DUCT ANAMOLY

Dr. K. Ramalingam, Dr. K. Sri Sowmya

Abstract :

Introduction–The incidence of mullerian duct anomalies is 0.5–5% , of which uterus didelphys/double uterus is rarest of all anomalies.Knowledge on them is important as they have great impact on women’s quality of life. Case Report–A 15 year old unmarried girl admitted in the Departement of OBGY , NRI hospital,guntur with pain abdomen of one month duration. Her cycles are regular with severe dysmenorrhoea. USG and MRI pelvis revealed Two uterine horns with two endometrial cavities, two cervical canals with obstructed left horn with hematometra of size 16.5*5.5cm with hematotrachelos, hematosalphinx with absent left kidney. Laparotomy was done and drianage of hematometra , excision of left sided cervix, uterine horn and fallopian tube with fimial cyst was done. Postoperatively, patient was relieved of her symptoms. Discussion – Mullerian duct anamolies occur due to abnormal emyological development of mullerian duct. They often associated with renal anamolies. They present with amenorrhoea,severe dysmenorrhoea and palpable mass due to underlying hematotrachelometra. Association of uterine didelphys with renal agenesis and obstructed hemi vagina is called Herlyn–Werner–Wunderlisch syndrome, and our case is variant of it. Conclusion – Early and accurate diagnosis is vital because untreated cases may develop retrograde tubal reflux , endometriosis, impaired fertility and obstetric complications in later life.