A RARE CASE OF BILIARY ATRESIA WITH IT‘S COMPLICATION OF PORTAL HYPERTENSION: A CASE REPORT

Dr. Dhwani Upadhya; Dr. Nirali Patel; Dr. Jainex Patel

Volume : VII, Issue : II, February - 2018

A RARE CASE OF BILIARY ATRESIA WITH IT‘S COMPLICATION OF PORTAL HYPERTENSION: A CASE REPORT

Dr. Dhwani Upadhya, Dr. Nirali Patel, Dr. Jainex Patel

Abstract :

Biliary atresia (BA) is a progressive, idiopathic, fio–obliterative disease of the extrahepatic biliary tree that presents with biliary obstruction exclusively in the neonatal period. It has been listed as a rare disease by the Office of Rare Diseases (ORD) of the National Institutes of Health (NIH) – the incidence is as low as only 1 patient in 10,000 to 20,000 live births. However, Biliary Atresia is the most common surgical cause of neonatal jaundice for which Liver Transplantation is indicated. We report a rare case of Biliary Atresia in a 6 months old female child who presented with jaundice and abdominal distension.