A retrospective study of morphological types, surgical outcome and follow up of Total Anomalous Pulmonary Venous Connection, at our institute

Dr Balaji Aironi; Dr Rohit Shahapurkar; Dr Ninad Kotkar; Dr N B Agrawal

Volume : V, Issue : IX, September - 2016

A retrospective study of morphological types, surgical outcome and follow up of Total Anomalous Pulmonary Venous Connection, at our institute

Dr Balaji Aironi, Dr Rohit Shahapurkar, Dr Ninad Kotkar, Dr N B Agrawal

Abstract :

Total Anomalous Pulmonary Venous Connection was first, described by Wilson in 1798, where there is no direct communication between pulmonary veins and the left atrium. Rather all pulmonary veins are connected to right atrium or any of its tributaries. Only 1.5 – 3 % of all the Congenital Heart Diseases have TAPVC�s. Atrial Septal Defect is necessary for survival after birth. The site where the pulmonary veins connect the systemic veins is usually obstructed, resulting in severe pulmonary hypertension. Patients are often critically ill especially if obstruction is present. The median survival rate for Supra–cardiac and Cardiac TAPVC�s are 2.5 and 3 months respectively and Infra–cardiac have only 3 weeks of median survival. Surgical mortality is very high ranging from 2–20% with early mortality 12%. Hereby, we present our experience with TAPVC from 2007 to 2015 with aims to evaluate the morphology and surgical outcome pertaining to the anatomy