Volume : VI, Issue : IV, April - 2017

AGGRESSIVE FIBROMATOSIS WITH BONE INVOLVEMENT A CASE REPORT

Dr K S Raja, Dr M Ravi

Abstract :

 Aggressive fiomatosis is a condition marked by the presence of fioblasts, which are benign, slow–growing musculo–aponeurotic tumours with no evidence of any metastatic potential6. It is known to involve muscle, subcutaneous tissue and neurovascular structures. However, bone involvement is very rare1. We have presented the case report of a 13 year old boy with aggressive fiomatosis in the left gluteal region involving acetabulum, ilium and ischium. Clinical examination revealed a firm swelling about 9x7x3 centimetres in the lower outer quadrant of left gluteal region. Routine haematological and radiological investigations were performed. Complete blood count and ESR were normal. X–ray pelvis with both hips revealed an osteolytic lesion in the left ilium and ischium. Computed Tomography showed geographic, lytic lesions involving the supra acetabular region of left ilium and a part of ischium. CT scan guided FNAC showed degenerated osteocytes with occasional osteoclast giant cells with few inflammatory mononuclear cells. MRI showed a soft tissue mass adjacent to the left iliac wing. The differential diagnoses were chronic osteomyelitis, eosinophlic granuloma, cystic type of fious dysplsia. We did a wide local excision of the tumour with curettage of the surrounding bone. Histopathological examination of the specimen was suggestive of aggressive fiomatosis. In our two years of follow up the patient did not show any signs of recurrence. This case is being reported for its rarity since fiomatosis involving the bone is an unusual event.

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Article: Download PDF   DOI : 10.36106/ijsr  

Cite This Article:

Dr K S Raja, Dr M Ravi, AGGRESSIVE FIBROMATOSIS WITH BONE INVOLVEMENT A CASE REPORT, INTERNATIONAL JOURNAL OF SCIENTIFIC RESEARCH : VOLUME-6 | ISSUE-4 | APRIL‾2017


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