An Unusual Case of Clear Cell Sarcoma in  Adult

Juhi Singhala; Avanish Saxena; Pallav Agrawal; Manish Budhiraja; Anoop Kumar Singh

Volume : II, Issue : IV, April - 2013

An Unusual Case of Clear Cell Sarcoma in Adult

Juhi Singhala, Avanish Saxena, Pallav Agrawal, Manish Budhiraja, Anoop Kumar Singh

Abstract :

Clear cell sarcoma of the kidney is an uncommon renal neoplasm of childhood. It represents one of the most unfavorable tumors included in National Wilms� Tumor Study Group clinical protocols. Clear cell renal sarcoma is a rare tumor and comprises 4% of primary pediatric malignant renal tumors. It is known as an aggressive tumor with poor prognosis. We came across this rare tumor in an adult female (21 years-old). The case report is followed by discussion, stating the differentiating features between Wilms� and clear cell sarcoma, histological details, treatment, and prognosis. Clinically and radiographically, it resembles Wilms� tumor.