Atypical Variant of Motor Neuron Disease (Vulpian Bernhardt/ Flail Arm) - A case series

Dr. Dinesh Chaudhari; Dr. Pushpendra N Renjen; Dr Anjali Mishra; Dr Abhas Kumar

Volume : VIII, Issue : IX, September - 2019

Atypical Variant of Motor Neuron Disease (Vulpian Bernhardt/ Flail Arm) - A case series

Dr. Dinesh Chaudhari, Dr. Pushpendra N Renjen, Dr Anjali Mishra, Dr Abhas Kumar

Abstract :

Flail arm syndrome (FAS) has a similar clinical course and pathological findings as amyo¬trophic lateral sclerosis (ALS). It is important to distinguish the two diseases because FAS patients have significantly better survival rates compared with other typical ALS variants. Patients with FAS present with predominantly proximal, progressive and symmetric wasting and paresis of the upper limb (UL) muscles, while lower limbs (LL) und bulbar muscles are spared. FAS patients seem to show a prolonged survival compared to other ALS subtypes. In this article we will discuss about two such cases of Flail arm syndrome (FAS), who had better prognosis.