Volume : VIII, Issue : VII, July - 2019

Dyke–Davidoff– Masson Syndrome

Gowthami M, Athira P M, Kuku Mariam Suresh, Rachegowda. N

Abstract :

Dyke–Davidoff–Masson syndrome (DDMS) is a rare disorder characterized by recurrent seizures, facial asymmetry, contralateral hemiplegia, radiologic features of cereal hemiatrophy, and ipsilateral compensatory hypertrophy of the skull bone and sinuses due to cereal injury that may occur in early childhood or fetal life. We describe two cases of DDMS, who initially presented with refractory seizures to the departments of Pediatrics and Medicine at Sri Devaraj Urs Medical College and Hospital. First case is of a 12 year old male with right hemiparesis and seizures since 3 months, CT & MRI ain revealed diffuse mild atrophy with paucity of white matter in the left cereal hemisphere involving ipsilateral thalamus and midain, left cereal hemiatrophy and chronic left MCA infarct with adjacent gliotic changes. Another case is of 35–year–male referred for right hemiplegia and uncontrolled seizures for 5 years, CT ain revealed thickening of cranial vault, pneumatosis dilatans of bilateral frontal sinuses, left cereal hemiatrophy, and right cerebellar infarct and pneumatoencephalographic changes. In each case, the clinical features were noted along with computed tomography or magnetic resonance imaging which helped in confirming the diagnosis of DDMS. Therefore DDMS should also be considered as a differential diagnosis of refractory seizures.

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Article: Download PDF   DOI : 10.36106/ijsr  

Cite This Article:

DYKE-DAVIDOFF- MASSON SYNDROME, Gowthami M, Athira P M, Kuku Mariam Suresh, Rachegowda. N INTERNATIONAL JOURNAL OF SCIENTIFIC RESEARCH : Volume-8 | Issue-7 | July-2019

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