Volume : VII, Issue : XI, November - 2018
Kartagener Syndrome- A clinical dilemma
Dr. Karan Bagga, Dr. Monarch Shah, Dr. Anjali Kale
Abstract :
Kartagener syndrome is a subset of primary ciliary dyskinesia, an autosomal recessive condition characterized by abnormal ciliary structure and/or function leading to impaired mucociliary clearance. The prevalence of primary ciliary dyskinesia is approximately 1/12,000–1 /60,000[1]. Approximately 50% of the patients with primary ciliary dyskinesia have Kartagener syndrome/situs abnormality. No gender predilection is recognized. Kartagener syndrome is characterized by the clinical triad of situs inversus, chronic sinusitis and/or nasal polyposis and onchiectasis. We describe a case wherein the patient had an initial presentation suggestive of onchial asthma which turned out to be something out of the box. The symptoms described in our report will be commonly encountered by most paediatricians in their day to day practice
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DOI : 10.36106/ijsr
Cite This Article:
Kartagener Syndrome- A clinical dilemma , Dr. Karan Bagga, Dr. Monarch Shah, Dr. Anjali Kale , INTERNATIONAL JOURNAL OF SCIENTIFIC RESEARCH : Volume-7|Issue-11| November-2018
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Kartagener Syndrome- A clinical dilemma , Dr. Karan Bagga, Dr. Monarch Shah, Dr. Anjali Kale , INTERNATIONAL JOURNAL OF SCIENTIFIC RESEARCH : Volume-7|Issue-11| November-2018
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