IJSR - International Journal of Scientific Research

Dr. Chaitali Parekh; Dr. Manisha Joshi; Dr. Anagha Joshi; Dr Viral Panchal

Volume : VI, Issue : IV, April - 2017

OHVIRA syndrome: Imaging in diagnosis in an asymptomatic newborn case report

Dr. Chaitali Parekh, Dr. Manisha Joshi, Dr. Anagha Joshi, Dr Viral Panchal

Abstract :

OHVIRA (Obstructed hemivagina and ipsilateral renal agenesis) syndrome also known as Herlyn–Werner–Wunderlich syndrome is a rare congenital anomaly of the female urogenital tract involving both Mullerian and Wolffian ducts, characterized by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis. It usually presents and is diagnosed at puberty due to non–specific symptoms of pelvic pain with or without a pelvic or vaginal mass shortly following menarche. We present a case of this rare anomaly diagnosed in the first week of post–natal life by using imaging modalities like USG and MRI in a female neonate with no clinical symptoms.