IJSR - International Journal of Scientific Research

Geetika Sindhwani; Abhinav Jain; Manali Arora; Viral Patel; Shabnam Bhandari; Anju Ranga

Volume : VI, Issue : IX, September - 2017

ORIGINAL ARTICLE OF RENAL ANGIOMYOLIPOMAS: SYNDROMIC ASSOCIATION, RADIOLOGICAL DIVERSITY AND MANAGEMENT

Geetika Sindhwani, Abhinav Jain, Manali Arora, Viral Patel, Shabnam Bhandari, Anju Ranga

Abstract :

Introduction: Angiomyolipoma (AML) is a rare mesenchymal renal tumour with 80% sporadiac occurrence and 20% syndromic association with tuberous sclerosis complex (TSC).

This study aims at analyzing the spectrum of Renal Angiomyo–lipoma, their vivid presentations, and associated complications which are diagnosed using Ultrasonography and Computed Tomography thereby, facilitating treatment and determining prognosis.

Material

The above mentioned study was conducted in Department of Radiodiagnosis, VMMC and Safdarjung Hospital. Total of 10 patients with Ultrasound and CT suggestive of renal angiomyolipoma were included in study.

Results:

Mean age of presentation was 33.5±7 (28–40) years in association with Tuberous Sclerosis. All the patients of AML with associated Tuberous Sclerosis were females.

30% of all patients (3/10) presented with hypovolemic shock. Lesions were multiple and bilateral in 40 % (n=4) of patients.

Conclusion : Considerable amounts of fat in most lesions, facilitate diagnosis using CT or MRI. Tuberous sclerosis is associated with female predilection, multiplicity, bilaterality, more bleeding propensity and heterogeneity of AML lesions.