Volume : VI, Issue : IV, April - 2017

PANSCLEROTIC MORPHOEA WITH PSEUDOAINHUM A CASE REPORT

Dr V Gomathi, Dr K Narashimman

Abstract :

 Pansclerotic morphoea is a rare and severe disabling form of morphoea with the onset usually in children below the age of 14 years1. It is characterized by sclerosis of the skin, subcutis, fascia, muscle and even bone, associated with contracture, deformity, joint stiffness and growth retardation. This form has an aggressive course but spontaneous remission can occur in some cases2. We report a case of 9 old year girl with tautness of the skin, involving the right foot and leg with stiffness of the ankle and knee joints and deformity of the right foot, associated with a constriction ring involving the right 3rd toe. Clinical examination revealed a linear, indurated  plaque extending from right foot up to upper 3rd of the leg with deformity of right foot and knee and joint stiffness. She also had a pseudoainhum involving the right 3rd toe. The activity of the disease was assesed by histopathological examination, relevant blood examination–eosinophilia, elevated ESR5, and with radiological examination which showed soft tissue edema and bony involvement. The patient was started on low dose methotrexate. She showed little improvement with treatment. The case is being reported for in view of its rare occurrence.

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Article: Download PDF   DOI : 10.36106/ijsr  

Cite This Article:

Dr V Gomathi, Dr K Narashimman, PANSCLEROTIC MORPHOEA WITH PSEUDOAINHUM A CASE REPORT , INTERNATIONAL JOURNAL OF SCIENTIFIC RESEARCH : VOLUME-6 | ISSUE-4 | APRIL‾2017


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