Perceptual challenges in auditory  neural processing in neurodegenerative  conditions like Fredereich Ataxia

Mr. Ayas Muhammed; Ms. Archana; Dr. Rajashekhar

Volume : I, Issue : II, July - 2012

Perceptual challenges in auditory neural processing in neurodegenerative conditions like Fredereich Ataxia

Mr. Ayas Muhammed, Ms. Archana, Dr. Rajashekhar

Abstract :

Friedreich ataxia (FA) is considered as a neurodegenerative disorder and is the most frequent type of hereditary ataxia. FA is characterized by degeneration in several spinal tracts, dorsal roots and peripheral nerves. Due to the disruption in the neural function, these individuals pose certain perceptual challenges in understanding speech in the presence of noise. Auditory nerve is considered as an important structure for the neural processing of acoustic sounds. Any eak down in its function will result in auditory processing deficits. These difficulties can only be identified with detailed test battery approach which includes both behavioural and electrophysiological tests. Therefore in the present case study, we aim to highlight the auditory processing deficits in FA which resulted in the identification of auditory neuropathy spectrum disorder (ANSD) a rare neural disorder seen in individuals with FA. Further it sheds light in to the possible management options in individual with ANSD.