Peutz-Jeghers Syndrome With Recurrent Intussusception- Our Experience

Subramanyam VN; Vinay RP; Aswin K; Sireesha KR

Volume : VII, Issue : VIII, August - 2018

Peutz-Jeghers Syndrome With Recurrent Intussusception- Our Experience

Subramanyam Vn, Vinay Rp, Aswin K, Sireesha Kr

Abstract :

Peutz–Jeghers‘ syndrome (PJS) is an autosomal dominant disease, which is characterized by mucocutaneousmelanin pigmentation and multiplegastrointestinal polyps (hamartomatous). The gastrointestinal polyp backdrop may act as lead point for intussusception. Attempt at surgical intervention may need multiple resections leading to short bowel syndrome, adding to morbidity in these cases. We are herewith presenting a case of Puetz –Jeghers syndrome with recurrent intussusception.