Russell-Silver Syndrome - A rare case report

DR.A.VASANTHAKUMARI; DR.I.JAI GANESH; DR.K.VIVEK; DR.VIVEK REDDY; DR.S.LOKESH

Volume : VII, Issue : VIII, August - 2018

Russell-Silver Syndrome - A rare case report

Dr. A. Vasanthakumari, Dr. I. Jai Ganesh, Dr. K. Vivek, Dr. Vivek Reddy, Dr. S. Lokesh

Abstract :

Russell–Silver Syndrome (RSS) is a hetergenous syndrome which is characterized by severe intrauterine and postnatal growth retardation and typical dysmorphic features. The clinical picture is extremely diverse due to numerous diagnostic features reflecting a heterogeneous genetic disorder. It is a syndromic disorder present at birth that involves poor growth, low birth weight, short stature and differences in the size of the two sides of the body. This case report presents a dental management of an eleven year old female patient with Russell–Silver Syndrome