Undifferentiated Embryonal Sarcoma of Liver in a Child : A Rare Case Report

Dr. Suchita Patel; Dr. Dhaval Jetly; Dr. Shailee Mehta; Dr. Priti Trivedi

Volume : VIII, Issue : XII, December - 2019

Undifferentiated Embryonal Sarcoma of Liver in a Child : A Rare Case Report

Dr. Suchita Patel, Dr. Dhaval Jetly, Dr. Shailee Mehta, Dr. Priti Trivedi

Abstract :

Undifferentiated Emyonal Sarcoma of Liver (UESL) is a rare and highly malignant primary hepatic tumor of mesenchymal origin. We present a case of Primary UESL in 14 year old female, presenting with a painful swelling in right hypochondrium and jaundice. CT Scan revealed a 18cm mass involving segment V and VIII of liver. Core needle Biopsy revealed proliferation of pleomorphic spindle cells with few interspersed rhabdoid cells. Immunohistochemical staining revealed tumor cells were immunopositive for Vimentin and Desmin, rendering it to be a UESL. Total resection with preoperative or postoperative radiochemotherapy is currently considered to be the key approach for improving the survival rate.Thus, UESL is a rare hepatic tumor,but an early diagnosis and prompt treatment may be useful in improving patients survival rate.