Unilateral myelinated retinal nerve fibers associated with ipsilateral myopia and amblyopia in a 2yearold boy

Shinji Makino

Volume : V, Issue : IX, September - 2016

Unilateral myelinated retinal nerve fibers associated with ipsilateral myopia and amblyopia in a 2yearold boy

Shinji Makino

Abstract :

A 2–year–old boy presented with exotropia and diminished vision in his right eye. His best–corrected visual acuity was 20/1400 and 20/94 in the right and left eyes, respectively. Cycloplegic refraction was S–10.75D C– 1.25D100 and S+1.00D C+1.00D80 in the right and left eye, respectively. Fundus examination revealed extensive myelinated retinal nerve fibers in the right eye. In addition, a hypoplastic optic disc was also observed in the right eye. The axial length was 25.22 mm and 21.30 mm in the right and left eyes, respectively. The patient was started amblyopic treatment, which included prescription of full cycloplegic refraction. However, it was difficult for him to wear the refractive corrected spectacle glasses. We should be aware of the limited prognosis and appropriate counseling for patients and their families is important in this rare condition.