A RARE ASSOCIATION OF BILATERAL STARGARDT‘S DISEASE WITH BILATERAL KERATOCONUS

Dr S Anuradha; Dr B Latha; Dr C Sony Shireesha; Dr M Sushma

Volume : IX, Issue : X, October - 2019

A RARE ASSOCIATION OF BILATERAL STARGARDT‘S DISEASE WITH BILATERAL KERATOCONUS

Dr S Anuradha, Dr B Latha, Dr C Sony Shireesha, Dr M Sushma

Abstract :

PURPOSE: To report a case of rare association of bilateral stargardt’s disease with bilateral keratoconus Methods:A 33year old male presented with bilateral progressive vision loss with BCVA of counting fingers at 3 metres in right eye and at 1 metre in left eye.On examination corneal ectasia with thinning,vogt’sstriae and munson’s sign were observed. Scissoring reflex was seen on retinoscopy.Hence corneal topography was done with k values 57.3x59˚ in right eye and 59x149˚ in the left eye and pupils were round,regular,reacting to slight. On fundus examination,retinal pigment epithelial changes of Beaten Bronze appearance were observed characteristic of stargardt’s disease Results:High k values on corneal topography suggestive of Keratoconus and retinal pigment epithelial changes suggestive of stargardt’s disease Conclusion:After an intense search, the association of keratoconus and stargardt’s has not yet reported so far, hence it is a rare association