A Rare Case of Papillon Lefevre Syndrome Associated with Primary Bronchiectasis

Dr. DIGUVINTI SREERAMULU; Dr. P.C.VASANTHA RAO; Dr. CHENNAKESAVULU DARA

Volume : III, Issue : VII, July - 2014

A Rare Case of Papillon Lefevre Syndrome Associated with Primary Bronchiectasis

Dr. Diguvinti Sreeramulu, Dr. P. C. Vasantha Rao, Dr. Chennakesavulu Dara

Abstract :

Papillon Lefevre Syndrome is a rare autosomal recessive syndrome that appears in childhood, characterized by diffuse transgredient Palmoplantarkeratoderma(PPKD) and aggressive periodontitis in both primary and secondary dentition with recurrent pyogenic infections. We report a rare case is associated with primary onchiectasis which has not been reported so far to our knowledge.